A 28-year-old man presents with unilateral peripheral retinal vascular sheathing, temporal dragging of the macula, and a history of poor vision since childhood in that eye. Fundoscopy shows straightening of the temporal vasculature. What is the most likely diagnosis?

• A Retinopathy of prematurity
• B Coats disease
• C Sickle cell retinopathy
• D Familial exudative vitreoretinopathy (FEVR) ✓

Explanation

FEVR classically presents with temporal dragging of the retina, straightening of the temporal vasculature, and peripheral avascular retina, often mimicking ROP but in full-term patients. ROP (option A) occurs in premature infants. Coats disease (option B) shows telangiectasia and exudation without vascular dragging. Sickle cell retinopathy (option C) shows sea-fan neovascularization and has a different fundus pattern.

Reference: Kanski's Clinical Ophthalmology, 9th ed.

High-yield for: NEET PGINI-CETNExTFMGEUSMLEPLABMRCP

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