Which chest radiographic finding is most characteristic of Ebstein anomaly?

• A Boot-shaped heart with concave pulmonary bay
• B Straightening of the left heart border with double density
• C Snowman configuration of the superior mediastinum
• D Giant right atrium producing a box-shaped cardiomegaly ✓

Explanation

Downward displacement of the tricuspid valve in Ebstein anomaly atrialises a portion of the right ventricle, producing massive right atrial enlargement and a box-shaped or globular cardiomegaly with reduced pulmonary vascularity. The snowman configuration belongs to supracardiac total anomalous pulmonary venous connection, which is the key fact killing option C.

Reference: Grainger and Allison's Diagnostic Radiology, 7th ed.

High-yield for: NEET PGINI-CETNExTFMGEUSMLEPLABMRCP

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