Superior semicircular canal dehiscence (SSCD) presents with which of the following characteristic symptom combination?

• A Pulsatile tinnitus, autophony, and sound-induced vertigo (Tullio phenomenon) ✓
• B Episodic vertigo with aural fullness and low-frequency SNHL
• C Progressive unilateral SNHL with facial nerve palsy
• D Sudden bilateral SNHL with systemic autoimmune disease

Explanation

Superior semicircular canal dehiscence (Minor's syndrome) results from a bony defect in the superior canal, creating a third mobile window. This causes hyperacusis for bone-conducted sounds, autophony (hearing one's own voice abnormally loudly), pulsatile tinnitus, and Tullio phenomenon (sound-induced vertigo and oscillopsia). Audiometry shows a characteristic air-bone gap in low frequencies with normal acoustic reflexes. Meniere's disease (option B) has aural fullness and low-frequency SNHL but not autophony. Progressive SNHL with facial palsy suggests acoustic neuroma or temporal bone cholesteatoma.

Reference: Dhingra Diseases of Ear, Nose and Throat, 7th ed.

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Written and medically reviewed by the StethoPrep medical team.